Cervical spondylotic amyotrophy presenting as dropped head syndrome

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dc.contributor.author Ahdab, Rechdi
dc.contributor.author Creange, Alain
dc.contributor.author Benaderette, Sandrine
dc.contributor.author Lefaucheur, Jean-Pascal
dc.date.accessioned 2019-04-10T07:25:41Z
dc.date.available 2019-04-10T07:25:41Z
dc.date.copyright 2009 en_US
dc.date.issued 2019-04-10
dc.identifier.issn 1872-6968 en_US
dc.identifier.uri http://hdl.handle.net/10725/10391
dc.description.abstract We report a case of acute-onset dropped head syndrome in a 65-year-old patient in whom the diagnosis of amyotrophic lateral sclerosis (ALS) was initially proposed based on electromyographic signs of neck and shoulder muscle denervation. There were no signs of pyramidal involvement and the clinical and electromyographic signs of motor denervation never evolved beyond the neck and shoulder girdle muscles after a 6-year follow-up period, which argued against ALS. Other causes of dropped head syndrome were carefully ruled out based on clinical findings, electrodiagnostic studies and blood investigations. The restriction of muscle denervation to a few cervical myotomes, the presence of C3–C4 spondylotic changes without associated root or spinal cord compression, and the absence of an alternative explanation to the patient's symptoms strongly supported the diagnosis of cervical spondylotic amyotrophy (CSA). CSA is thought to result from spinal cord microcirculatory disturbances and secondary anterior horn cell degeneration due to ischemia. Our case enlarges the clinical spectrum of focal cervical anterior horn disease, which classically results in more distal monomelic atrophy affecting one or both upper limbs. en_US
dc.language.iso en en_US
dc.title Cervical spondylotic amyotrophy presenting as dropped head syndrome en_US
dc.type Article en_US
dc.description.version Published en_US
dc.author.school SOM en_US
dc.author.idnumber 201100314 en_US
dc.author.department N/A en_US
dc.description.embargo N/A en_US
dc.relation.journal Clinical Neurology and Neurosurgery en_US
dc.journal.volume 111 en_US
dc.journal.issue 10 en_US
dc.article.pages 874-876 en_US
dc.keywords Amyotrophic lateral sclerosis en_US
dc.keywords Anterior horn cell en_US
dc.keywords Cervical spine en_US
dc.keywords Cervical spondylotic amyotrophy en_US
dc.keywords Dropped head en_US
dc.identifier.doi https://doi.org/10.1016/j.clineuro.2009.07.005 en_US
dc.identifier.ctation Ahdab, R., Créange, A., Benaderette, S., & Lefaucheur, J. P. (2009). Cervical spondylotic amyotrophy presenting as dropped head syndrome. Clinical neurology and neurosurgery, 111(10), 874-876. en_US
dc.author.email rechdi.ahdab@lau.edu.lb en_US
dc.identifier.tou http://libraries.lau.edu.lb/research/laur/terms-of-use/articles.php en_US
dc.identifier.url https://www.sciencedirect.com/science/article/pii/S0303846709001735 en_US
dc.author.affiliation Lebanese American University en_US

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